Congenital pulmonary valvular and infundibular stenosis complicating Ebstein's anomaly of the tricuspid valve. A case report.
نویسندگان
چکیده
Clinical, hemodynamic, angiographic, and echocardiographic as well as operative findings of a 19 years old girl are presented who had the unique combination of severe pulmonary valvular and infundibular stenosis with Ebstein's anomaly of the tricuspid valve. Pulmonary stenosis was relieved by infundibular resection and valvotomy. The atrial septal defect was closed with plication of atrialized ventricle and insertion of a porcine tricuspid prosthesis. Recatheterization 2 months postoperatively revealed disappearance of characteristic angiographic findings and slight residual gradient.
منابع مشابه
Ebstein's Anomaly Associated with Cardiomyopathy
DURING the past decade definite progress has been made toward an understanding of the hemodynamic alterations and pathophysiologic aspects of Ebstein's anomaly of the tricuspid valve.1' 2 Moreover, an increased awareness of the characteristic clinical findings has resulted in an apparent increase in incidence of the disease. Largely as a result of careful pathologic studies, atypical forms of E...
متن کاملPercutaneous transcatheter valve-in-valve implantation with the balloon-expandable valve for the treatment of a dysfunctional tricuspid bioprosthetic valve: a pediatric case report.
An inverted Edwards SAPIEN 23 mm valve was implanted in a 14-year-old patient with Ebstein's anomaly who received a Medtronic Mosaic 25 mm valve 8 years earlier and presented with significant progressive symptoms related to severe valvular regurgitation and moderate stenosis. The procedure was performed via the femoral vein using the RetroFlex 3 system and predilatation of the tricuspid valve, ...
متن کاملEbstein's Anomaly Associated with Cardiomyopathy and Pulmonary Hypertension.
DURING the past decade definite progress has been made toward an understanding of the hemodynamic alterations and pathophysiologic aspects of Ebstein's anomaly of the tricuspid valve.1' 2 Moreover, an increased awareness of the characteristic clinical findings has resulted in an apparent increase in incidence of the disease. Largely as a result of careful pathologic studies, atypical forms of E...
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Background and Aims: Ebstein’s anomaly is an abnormal displacement downward of Tricuspid valve into the right ventricular, which is accompanied by myopathy of the right ventricular. It is found rarely with the prevalence of approximately 1:20000. Since the diagnosis of this disease in the appropriate position and time, the management of patients is important. This infant with Ebstein’s anomaly ...
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Enlargement of right atrium is usually secondary to pulmonary hypertension due to valvular heart diseases or obstructive pulmonary disorders, atrial septal defect, tricuspid atresia or stenosis, pulmonary stenosis, primary pulmonary hypertension, Ebstein's anomaly. Congenital enlargement of right atrium is rare and it commonly presents in children. Our patient presented with congenital giant ri...
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عنوان ژورنال:
- Japanese heart journal
دوره 21 6 شماره
صفحات -
تاریخ انتشار 1980